巨细胞性动脉炎

定义 英文原文（暂无中文）

A rare vasculitis characterized by mostly unilateral inflammation of the temporal artery affecting patients up to fifty years of age. Patients typically present with a lump in the temporal region or a prominent temporal artery and often have headaches. Males are more frequently affected than females, and major systemic symptoms, ocular complications, and a biological inflammatory syndrome are usually absent, although peripheral blood eosinophilia may be seen. Histopathological analysis shows arteritis predominantly of the intima with possible extension to the perivascular tissue. The presence of granuloma, giant cells or fibrinoid necrosis is rare. Clinical relapses after one episode are uncommon.

别名

非巨细胞肉芽肿性颞动脉炎伴嗜酸性粒细胞增多症

基本事实

遗传方式

未知

发病年龄

儿童期

患病率

<1 / 1 000 000

临床表型 8

外部标识与链接