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中间葡萄膜炎

Intermediate uveitis

ORPHA:279914疾病

定义 英文原文(暂无中文)

A rare ophthalmic disorder characterized by intraocular inflammation primarily localized to the vitreous and peripheral retina. It incorporates pars planitis, posterior cyclitis, and hyalitis. Patients present with painless floaters, decreased or blurred vision, less frequently with pain, redness, and photophobia. On examination, snow banking, vitreous snowballs, peripheral retinal vascular sheathing, vitreous cells, and vitreous haze can be seen. Complications include epiretinal membrane formation, cataract formation, cystoid macular edema, or band keratopathy, among others. The condition may be idiopathic or occur in the context of infectious or systemic diseases.

别名

IU

基本事实

遗传方式
不适用
发病年龄
儿童期

临床表型 18

常见 79–30%1

  • 黄斑水肿 HP:0040049

偶见 29–5%13

  • 前葡萄膜炎 HP:0012122
  • 带状角膜病 HP:0000585
  • 白内障 HP:0000518
  • 囊样黄斑水肿 HP:0011505
  • 视网膜前膜 HP:0100014
  • 青光眼 HP:0000501
  • 视神经炎 HP:0100653
  • 虹膜后粘连 HP:0011484
  • 视力下降 HP:0007663
  • 血管炎 HP:0002633
  • 玻璃体漂浮物 HP:0100832
  • 玻璃体混浊 HP:0030652
  • 雪球状玻璃体 HP:0030661

罕见 <4–1%4

  • 慢性感染 HP:0031035
  • 黄斑瘢痕 HP:0200056
  • 银屑病样皮炎 HP:0003765
  • 肾小管间质性肾炎 HP:0001970

外部标识与链接

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本页数据来源

  • 疾病定义、同义词、基因、表型、流行病学:Orphanet(CC BY 4.0)
  • 中文病名:Orphanet 中文包,冻结于 2020-06-01
  • 表型中文标签:HPO 简体中文翻译(CHPO 上游成果)