原发性皮肤浆细胞增多症

定义 英文原文（暂无中文）

A rare acquired skin disease characterized by benign proliferation of mature plasma cells with a typical triad of cutaneous lesions, polyclonal hypergammaglobulinemia, and superficial lymphadenopathy, without an apparent underlying cause. The skin lesions consist of multiple round-to-oval, red-to-dark-brown macules, papules, and plaques most commonly found on the trunk, but also the face, neck, and axillae.

基本事实

遗传方式

不适用

发病年龄

成年期、老年期

患病率

<1 / 1 000 000

外部标识与链接