表皮松解色素痣

定义 英文原文（暂无中文）

A rare nevus characterized by single or multiple non-inflammatory verrucous skin lesions composed of keratinocytes, often present from birth, and distributed along the lines of Blaschko. Histologically, the lesions show features of epidermolytic hyperkeratosis with perinuclear vacuolization of keratinocytes of the upper epidermis with coarse keratohyaline granules. There is no extra-cutaneous involvement. Affected individuals are at risk of parenting a child with bullous ichthyosiform erythroderma.

别名

表皮色素痣伴表皮松解型角化过度症

基本事实

发病年龄

各年龄段

患病率

>1 / 1000

外部标识与链接