罕见病知识库 RareSeen

阴唇癌

Pilomatrix carcinoma

ORPHA:499182疾病

定义 英文原文(暂无中文)

A rare skin tumor characterized by an asymptomatic, solitary, often ulcerated nodule most commonly located in the face, involving the deep dermis, subcutaneous tissue, and skeletal muscle and fascia. Histopathologically, the lesion is composed of aggregates of atypical basaloid cells with numerous mitoses. Typical features include shadow cells, keratin cysts, and trichohyalin and keratohyalin granules. The tumor is locally aggressive and shows a tendency to recur after incomplete excision. Regional lymph node or visceral metastasis has been reported.

别名

Malherbe钙化上皮癌

基本事实

遗传方式
不适用
发病年龄
青少年期、成年期、老年期

外部标识与链接

OrphanetMONDO:0003414ICD-10 C44.3、C44.4ICD-11 2C3YClinicalTrials.gov 检索

发现这一页有错误?告诉我 · 邮件主题会自动带上本页的 ORPHA 编号

本页数据来源

  • 疾病定义、同义词、基因、表型、流行病学:Orphanet(CC BY 4.0)
  • 中文病名:Orphanet 中文包,冻结于 2020-06-01
  • 表型中文标签:HPO 简体中文翻译(CHPO 上游成果)