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5-羟色胺分泌型胰腺神经内分泌肿瘤

Serotonin-producing neuroendocrine tumor of pancreas

ORPHA:506090疾病

定义 英文原文(暂无中文)

A rare functioning neuroendocrine tumor of pancreas characterized by a typically well-differentiated neoplasm composed of cells expressing serotonin. Patients may present with atypical carcinoid syndrome with abdominal pain, diarrhea, weight loss, and/or flushing. Carcinoid syndrome is usually present only when there are liver metastases. The tumors tend to be larger than non-functioning tumors and are associated with a poorer prognosis because they are almost always metastatic.

别名

Serotonin-producing PNET、Serotonin-producing pancreatic NET、Serotonin-producing pancreatic neuroendocrine tumor

基本事实

遗传方式
不适用

外部标识与链接

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本页数据来源

  • 疾病定义、同义词、基因、表型、流行病学:Orphanet(CC BY 4.0)
  • 中文病名:Orphanet 中文包,冻结于 2020-06-01
  • 表型中文标签:HPO 简体中文翻译(CHPO 上游成果)