胰腺混合性神经内分泌-非神经内分泌肿瘤
Mixed neuroendocrine and non-neuroendocrine neoplasm of pancreas
ORPHA:506112疾病
定义 英文原文（暂无中文）
A rare neuroendocrine neoplasm of pancreas characterized by morphologically recognizable neuroendocrine and non-neuroendocrine components, each constituting at least 30% of the tumor volume. Based on histopathology, mixed ductal- and mixed acinar-neuroendocrine carcinomas are distinguished. Patients usually present with unspecific symptoms related to tumor growth and/or metastasis, although occurrence of Zollinger-Ellison syndrome has been reported. Resectability of the tumor is the most important prognostic factor.
别名
MiNEN of pancreas、Pancreatic MiNEN、Pancreatic mixed neuroendocrine-nonneuroendocrine neoplasm
基本事实
- 遗传方式
- 不适用
外部标识与链接
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本页数据来源
- 疾病定义、同义词、基因、表型、流行病学：Orphanet（CC BY 4.0）
- 中文病名：Orphanet 中文包，冻结于 2020-06-01
- 表型中文标签：HPO 简体中文翻译（CHPO 上游成果）