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肝细胞癌合并胆管上皮癌

Combined hepatocellular carcinoma and cholangiocarcinoma

ORPHA:529852疾病

定义 英文原文(暂无中文)

A rare hepatic tumor characterized by the presence of both hepatocytic and cholangiocytic differentiation within a primary liver carcinoma. The lesion commonly arises in the context of chronic liver disease (such as hepatitis B or C, or steatohepatitis) or exposure to a variety of exogenous agents. Patients may present with signs and symptoms related to the tumor, as well as to the underlying condition. Typical manifestations include right upper quadrant abdominal pain, weight loss, hepatosplenomegaly, jaundice, and ascites. The entity has been associated with a worse prognosis than hepatocellular carcinoma after resection.

别名

Combined hepatocellular-cholangiocarcinoma

基本事实

遗传方式
不适用
发病年龄
成年期、老年期

外部标识与链接

OrphanetMONDO:0044791ICD-10 C22.0、C22.1ICD-11 2C12.00ClinicalTrials.gov 检索

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本页数据来源

  • 疾病定义、同义词、基因、表型、流行病学:Orphanet(CC BY 4.0)
  • 中文病名:Orphanet 中文包,冻结于 2020-06-01
  • 表型中文标签:HPO 简体中文翻译(CHPO 上游成果)