孤立性肠系膜静脉血栓
Isolated mesenteric vein thrombosis
ORPHA:583861疾病
定义 英文原文（暂无中文）
A rare intestinal disease characterized by isolated thrombosis of the mesenteric veins without involvement of the splenic or portal veins, potentially causing mesenteric ischemia. It may be primary/idiopathic or due to one or more local or systemic predisposing conditions, and may be acute/subacute or chronic, the latter being used for patients with symptoms lasting longer than 4 weeks but without bowel infarction, or patients without recent symptoms, where the thrombosis is an incidental finding. Symptoms depend on the extent and severity of thrombosis and often involve prolonged nonspecific abdominal complaints.
基本事实
- 遗传方式
- 不适用
- 发病年龄
- 成年期、老年期
- 患病率
- 1-9 / 100 000（Europe）
临床表型 19
极常见 99–80%2
- 腹痛 HP:0002027
- 肠系膜静脉血栓形成 HP:0030248
常见 79–30%5
- 厌食症 HP:0002039
- 腹泻 HP:0002014
- 白细胞增多症 HP:0001974
- 恶心 HP:0002018
- 呕吐 HP:0002013
偶见 29–5%12
- 腹胀 HP:0003270
- 循环淀粉酶浓度异常 HP:0410282
- 腹水 HP:0001541
- 胆管炎 HP:0030151
- 胆石症 HP:0001081
- 发热 HP:0001945
- 胃肠道出血 HP:0002239
- 低血压 HP:0002615
- 循环乳酸水平升高 HP:0002151
- 肠内气体 HP:6000377
- 脓毒症 HP:0100806
- 休克 HP:0031273
外部标识与链接
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本页数据来源
- 疾病定义、同义词、基因、表型、流行病学：Orphanet（CC BY 4.0）
- 中文病名：Orphanet 中文包，冻结于 2020-06-01
- 表型中文标签：HPO 简体中文翻译（CHPO 上游成果）