Neonatal compartment syndrome

定义 英文原文（暂无中文）

A rare non-inflammatory vasculopathy characterized by intracompartmental pressure typically in a distal upper extremity due to intrauterine ischemia and external compression. Affected limb presents significant swelling and sentinel skin changes (desquamation, blister/bullae formation, and skin necrosis). It can lead to long-term sequelae including Volkmann contracture, limb length discrepancies,bone growth abnormalities and nerve lesions. Neurologic involvement, ranging from sensory and motor nerve palsies to complete hand paralysis, may persist.

别名

CVIC、Congenital Volkmann ischemic contracture syndrome、NCS、Neonatal Volkmann ischemic contracture syndrome、Syndrome de Volkmann congénital

基本事实

遗传方式

不适用

发病年龄

新生儿期

患病率

<1 / 1 000 000

外部标识与链接