Splenic venous malformation
ORPHA:688523疾病暂无中文名
定义 英文原文(暂无中文)
A rare venous malformation characterized by splenic non-encapsulated, non-neoplastic vascular channels of varying sizes (ranging from capillaries to cavernous vessels) containing slow-flowing blood. The majority of patients are asymptomatic and the condition is usually discovered incidentally. When patients are symptomatic, they may present with dyspnea, abdominal pain, splenomegaly, diarrhea, or constipation. Lesions are usually benign with no malignant potential. However, very large lesions may require splenectomy due to their increased risk of rupture, which may lead to intra-abdominal hemorrhage.
别名
Splenic cavernous malformation、Splenic slow-flow venous malformation、Venous malformation of the spleen
基本事实
- 遗传方式
- 不适用
外部标识与链接
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本页数据来源
- 疾病定义、同义词、基因、表型、流行病学:Orphanet(CC BY 4.0)
- 中文病名:Orphanet 中文包,冻结于 2020-06-01;本条目在该版本中无中文名
- 表型中文标签:HPO 简体中文翻译(CHPO 上游成果)