结外鼻型NK/T细胞淋巴瘤

定义 英文原文（暂无中文）

Extranodal nasal NK/T cell lymphoma (NKTCL) is a rare, malignant neoplasm mainly affecting men in the fifth decade of life, that usually arises in the nose, paranasal sinuses, orbits or upper airway, and that can present with a nasal mass, nasal bleeding, nasal obstruction, palate perforation (i.e. midline perforation of the hard palate), and mid-facial and/or upper airway destructive lesions. In advanced disease stages, which are associated with a poor prognosis, NKTCL may disseminate to other organs. A few cases of NKTCL presenting primarily in the lymph nodes have also been described.

别名

鼻型T/自然杀伤细胞淋巴瘤

基本事实

遗传方式

多基因/多因素、不适用

发病年龄

成年期

患病率

1-9 / 100 000（France）

外部标识与链接