肠病相关T细胞淋巴瘤

定义 英文原文（暂无中文）

A rare T-cell non-Hodgkin lymphoma characterized by a neoplasm of intraepithelial T-cells mostly occurring in the jejunum or ileum in patients with celiac disease. The lesion may be multifocal and form ulcerating nodules, plaques, strictures, or an exophytic mass. The mesentery and mesenteric lymph nodes are commonly involved. Patients typically present with abdominal pain, malabsorption or diarrhea, anorexia, weight loss, fatigue, nausea, vomiting, and sometimes intestinal perforation or hemorrhage. Prognosis is generally poor.

别名

肠病型T-细胞淋巴瘤

基本事实

遗传方式

不适用

发病年龄

成年期

患病率

<1 / 1 000 000（United States）

外部标识与链接