指突状树突细胞肉瘤

定义 英文原文（暂无中文）

A rare dendritic cell tumor characterized by a neoplasm composed of spindle to ovoid cells with phenotypic features similar to those of interdigitating dendritic cells. Solitary lymph node involvement is common, although extranodal localization (in particular skin and soft tissue) has also been reported. Patients usually present with an asymptomatic mass, sometimes with systemic symptoms such as fatigue, fever, and night sweats. Generalized lymphadenopathy, splenomegaly, or hepatomegaly may be seen in rare cases. The clinical course is generally aggressive.

别名

指突状树突细胞肉瘤

基本事实

发病年龄

成年期

患病率

<1 / 1 000 000（Europe）

外部标识与链接