肝炎性假瘤
Inflammatory pseudotumor of the liver
ORPHA:90003疾病
定义 英文原文（暂无中文）
A rare benign liver tumor characterized by a prominent inflammatory infiltrate and often mimicking a malignant liver neoplasm. The tumor is frequently solitary with a predilection for the right lobe; however, multiple lesions are possible. There are two clinicopathological subtypes: fibrohistiocytic inflammatory pseudotumor of the liver and lymphoplasmacytic inflammatory pseudotumor of the liver. Patients present with non-specific clinical symptoms such as abdominal pain or discomfort, fever, and weight loss. The condition may be associated with other chronic inflammatory or autoimmune diseases.
基本事实
- 遗传方式
- 不适用
- 发病年龄
- 各年龄段
临床表型 17
必现 100%2
- 肝脏超声异常 HP:0031140
- 肝脏肿瘤 HP:0002896
常见 79–30%3
- 腹痛 HP:0002027
- 自身免疫性抗体阳性 HP:0030057
- 发热 HP:0001945
偶见 29–5%9
- 腹胀 HP:0003270
- 虚弱 HP:0025406
- 胆道异常 HP:0001080
- 肝硬化 HP:0001394
- 糖尿病 HP:0000819
- 乙肝病毒抗体水平升高 HP:0410369
- 恶心 HP:0002018
- 呕吐 HP:0002013
- 体重减轻 HP:0001824
罕见 <4–1%2
- 血清丙氨酸转氨酶升高 HP:0031964
- 血清天冬氨酸转氨酶升高 HP:0031956
排除 0%1
- 循环甲胎蛋白浓度升高 HP:0006254
外部标识与链接
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本页数据来源
- 疾病定义、同义词、基因、表型、流行病学：Orphanet（CC BY 4.0）
- 中文病名：Orphanet 中文包，冻结于 2020-06-01
- 表型中文标签：HPO 简体中文翻译（CHPO 上游成果）