红斑狼疮性脂膜炎
Lupus erythematosus panniculitis
ORPHA:90285疾病
定义 英文原文(暂无中文)
A rare form of chronic cutaneous lupus erythematosus characterized by recurrent, indurated, erythematous plaques and subcutaneous nodules with normal overlying epidermis, occurring predominantly on the face, upper arms, trunk, buttocks, and thighs. The lesions can ulcerate and lead to scarring. Histological findings include lobular lymphocytic panniculitis, hyaline fat necrosis, mucin deposition, and calcification. The condition may be associated with discoid or systemic lupus erythematosus.
别名
深部红斑狼疮
基本事实
- 发病年龄
- 青少年期、成年期、儿童期、老年期、婴儿期
- 患病率
- <1 / 1 000 000(United States)
外部标识与链接
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本页数据来源
- 疾病定义、同义词、基因、表型、流行病学:Orphanet(CC BY 4.0)
- 中文病名:Orphanet 中文包,冻结于 2020-06-01
- 表型中文标签:HPO 简体中文翻译(CHPO 上游成果)